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영남의대학술지 Vol.24_No.2 Suppl. P.S710-718, Dec. 2007

Case Report

선천성 질 무발생 환자 2 예

Two Cases of Congenital Vaginal Absence

박성철, 신현진*, 김효헌**, 이태형, 이승호, 이두진
영남대학교 의과대학 산부인과학교실?
영남대학교 의료공학연구소*
영남대학교 의과대학 성형외과학교실**
책임저자:이두진, 대구광역시 남구 대명 5동 317-1. 영남대학교 의과대학 산부인과학교실
Tel: (053) 620-3435. Fax: (053) 654-0676
E-mail: djlee@med.yu.ac.kr.

December 30, 2007

Abstract

Congenital absence of vagina(Mayer-Rokitansky-Kuster-Hauser syndrome) is found between 1 in 4,000 and 20,000 female births, and is frequently associated with various urinary tract and skeletal anomalies. As the patients have normal ovarian functions, they appear as normal female phenotype and have normal female karyotype 46, XX. Inability of coitus is one of the main problems they have, so the goal of treatment is to create a vagina adequate to allow sexual activity. Both surgical and nonsurgical approaches have been utilized. The authors experienced two cases of congenital absence of vagina successfully treated by surgical and nonsurgical method.

Key Words: Congenital absence of vagina, Ingram method, McIndoe operation

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