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영남의대학술지 Vol.24_No.2 Suppl. P.S689-695, Dec. 2007

Case Report

Hemiconvulsion-Hemiplegia-Epilepsy 증후군 1 예

A Case of Hemiconvulsion-Hemiplegia-Epilepsy Syndrome

문한구
영남대학교 의과대학 소아과학교실
책임저자:문한구, 대구광역시 남구 대명5동 317-1, 영남대학교 의과대학 소아과학교실
Tel: (053) 620-3533, Fax: (053) 629-2252
Email: hkmoon@med.yu.ac.kr

December 30, 2007

Abstract

Hemiconvulsion-Hemiplegia-Epilepsy syndrome is characterized by a prolonged unilateral convulsion in the form of status producing a persisting hemiplegia during a febrile illness, followed by epilepsy. It occurs in a child, between 5 months and 4 years old, with a peak incidence during the first 2 years of life. Although the etiologies of this syndrome are diverse, preexisting asymptomatic lesion of perinatal or prenatal origin is found in a number of cases. I experienced a case of HHE syndrome in a 11 month old girl with abnormal perinatal history and developmental delay, who showed predominant right sided focal motor seizures followed by right hemiparesis.

Key Words: Hemiconvulsion-Hemiplegia-Epilepsy syndrome

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